Retroperitoneal Fibrosis: clinical case

Abstract

Fibrosis Retroperitoneal ( FRP ) is an infrequent disease once greasy retroperitoneal for fibers of collagen and inflammatory spy was characterized for the woven replacement, that he wraps up and compress to the structures retroperitoneales. Exist a primary form, Ormond´s disease, of proAsturian dialect autoimmune etiology and a secondary form, either malignant, due to reaction desmoplástica of the retroperitoneum in front of the infiltration for malignant cells, good for primary tumors retroperitoneals or metastásicos; Or else benign generally associated to aortic aneurysm abdominal although also it has happened to me that another one have been described multiple you cause . Clinically he becomes manifest for signs and due symptoms to structures's compression retroperitoneals and the right things to the toxic syndrome for the inflammatory process under way. TAC results in important the suspicion of FRPand in the secondary causes exclusion, however the biopsy once was opened represents the gold Standard in her diagnosis FRP. Actual treatment is surgical and/or pharmacologic (corticoids inmusupresores). her infrequent FRPmakes difficult the possibility of accomplishing studies randomizados and controlled. We present the recent manifested case of a patient with FRPclinically as a picture of footloose pain in straight flank of lift to moderated intensity; Where the imageries techniques, the exploratory Laparatomy with separation of the fibrous textile's straight ureter, ( ureterolysis ) and keys to establish diagnosis and treatment proved to be biopsy.